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Dysmorphology Presentations

17 topics

Overview

Presentations driven by body shape rather than mechanism: the face, head, hands, feet, limbs, stature, and skeleton. Organized by body region rather than by underlying biology so a clinician seeing "child with coarse face and short stature" has one place to start. Each entry leads with a region-specific reasoning frame, then a differential, then discriminating pearls and a work-up. Many of these patients also have metabolic or neurological findings; the body-region entry point is for "this is what I see first," not for "this is what is wrong."

Hands and feet

Polydactyly, syndactyly, limb reduction defects, arthrogryposis.

Head and face

Coarse facial features, hemifacial microsomia, craniosynostosis, hypertelorism, micrognathia, macroglossia, microtia.

Skeleton

Skeletal dysplasia (general approach), fractures with minimal trauma, hypermobile joints.

Stature and growth

Short stature, tall stature / overgrowth, hemihypertrophy / limb asymmetry, the dysmorphic newborn (general approach).