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Bayesian Risk Assessment

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Bayesian analysis updates a prior probability (based on pedigree or population data) with new conditional information (test results, family history, unaffected children) to calculate a posterior probability. It is one of the most useful quantitative tools in personalized risk assessment.

Hypothesis 1 (e.g., Carrier)Hypothesis 2 (e.g., Non-carrier)
Prior probabilityP(H1)P(H2)
Conditional probabilityP(evidence | H1)P(evidence | H2)
Joint probabilityPrior x ConditionalPrior x Conditional
Posterior probabilityJoint1 / (Joint1 + Joint2)Joint2 / (Joint1 + Joint2)

Example 1: Carrier risk updated by negative test

Problem: A woman has a 1/2 prior probability of being a carrier for CF. She undergoes carrier testing that detects 90% of pathogenic variants in her population. The test is negative. What is her updated carrier risk?

Solution:

CarrierNon-carrier
Prior1/21/2
Conditional (negative test)0.10 (10% of variants missed)1.00
Joint1/2 x 0.10 = 0.051/2 x 1.00 = 0.50
Posterior0.05 / 0.55 = 1/110.50 / 0.55 = 10/11
  • Updated carrier risk: 1/11 (approximately 9%)
  • The residual risk is 1/11, not zero, because the test does not detect all variants

Example 2: Combining family history with test results

Problem: A woman's brother has DMD. Her prior carrier risk is 1/2. She has 2 unaffected sons and a normal CK level (about two-thirds of carriers have elevated CK, so ~1/3 of carriers have a normal CK). What is her updated carrier risk?

Solution:

CarrierNon-carrier
Prior1/21/2
Conditional: 2 unaffected sons(1/2)^2 = 1/41
Conditional: normal CK1/31
Combined conditional1/4 x 1/3 = 1/121 x 1 = 1
Joint1/2 x 1/12 = 1/241/2 x 1 = 1/2
Posterior(1/24) / (1/24 + 1/2) = 1/1312/13
  • Updated carrier risk: 1/13 (approximately 8%)

Example 3: Prenatal/child risk for late-onset conditions

Problem: A 30-year-old man has a parent with Huntington disease (AD, 100% penetrance by age 70). The man is currently unaffected. What is his risk of carrying the variant?

Solution:

Carries HD variantDoes not carry
Prior1/21/2
Conditional (unaffected at 30)~0.85 (about 15% penetrant by 30)1
Joint1/2 x 0.85 = 0.4251/2 x 1 = 0.50
Posterior0.425 / 0.925 = 46%54%
  • His risk is slightly reduced from 50% to 46% because he is still unaffected at 30
  • As he ages without symptoms, his posterior risk continues to decrease
  • Prior probability: What you know before the new evidence. Comes from pedigree analysis, population frequencies, or inheritance patterns.
  • Conditional probability: How likely is the evidence under each hypothesis?
  • Residual risk: The posterior probability of being a carrier after a negative test. Never zero unless the test has 100% sensitivity.
  • Multiple pieces of evidence: Multiply the conditional probabilities together (they are independent observations)
  • Forgetting to use conditional probability for the alternative hypothesis: The conditional for non-carrier is usually 1 (certain to have a negative test, certain to have unaffected sons) but not always
  • Confusing sensitivity with detection rate: For carrier testing, the detection rate (proportion of variants detectable) is the relevant number, not analytical sensitivity
  • Not recognizing when Bayesian analysis is needed: Any time you have a prior risk AND new information, you should consider updating with Bayes